J Clin Neuromuscul Dis, 2014 · DOI: 10.1097/CND.0000000000000028 · Published: June 1, 2014
This paper discusses a case of monomelic amyotrophy (Hirayama disease) and its management. Usually, the disease's progression stops, leaving persistent arm weakness. Sometimes, symptoms improve with a cervical collar or surgery. The study focuses on a young man with monomelic amyotrophy. He was advised to avoid prolonged neck flexion without using a cervical collar. After a year of avoiding neck flexion, the patient's strength in his right finger extensors, finger flexors, and wrist extensors improved. This improvement helped him type and perform manual tasks more easily.
Avoidance of sustained neck flexion may be a viable conservative management strategy for monomelic amyotrophy.
Improved muscle strength can lead to enhanced ability to perform manual tasks and type.
Clinical improvement is possible even with radiologic signs of cervical cord compression, suggesting that surgery isn't always necessary